Interv Akut Kardiol. 2018;17(3):144-147 | DOI: 10.36290/kar.2018.013

Incidence and prognosis of patients with arrhythmogenic right ventricular dysplasia

David Šipula¹, Milan Kozák², Jiří Plášek¹, Miroslav Homza¹

¹ Kardiovaskulární oddělení, Fakultní nemocnice Ostrava

² Interní kardiologická klinika, Fakultní nemocnice Brno Bohunice

Objective: To monitor the proportion of patients with the diagnosis of arrhythmogenic right ventricular dysplasia (ARVD) indicatedfor ICD implantation.

Method: The authors describe the incidence of ARVD in a population during a six-year period and monitor the clinical manifestationsin patients with this diagnosis as well as the examination methods and, subsequently, the rate of arrhythmias.

Results: Our cohort comprised 6 patients with ARVD, with all of them having symptoms indicative of a haemodynamically significantventricular arrhythmia manifested by syncopal or presyncopal states. As evidenced by echocardiography, all the patientshad right ventricular dilation, which was confirmed by x-ray changes in 5 patients. These patients were indicated for implantablecardioverter defibrillator (ICD) placement according to the guidelines. During follow-up, haemodynamically significant ventriculararrhythmias were detected in 4 patients, of whom 3 patients were indicated for radiofrequency catheter ablation of a substratefrom the right ventricle due to recurrent ventricular arrhythmia.

Conclusion: Although a rare condition, the diagnosis of ARVD must be considered in patients with a history of syncope, presyncopalstates, or palpitations, particularly with exertion at a young age. In these patients, at least, radiographic and echocardiographicevaluation should be performed.

Keywords: arrhythmogenic right ventricular dysplasia, syncope, ICD implantation

Received: July 16, 2018; Accepted: July 16, 2018; Published: October 1, 2018  Show citation